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Hypoplastic left heart syndrome (HLHS)HHypoplastic left heart syndrome (HLHS)Hypoplastic left heart syndrome (HLHS)EnglishCardiologyChild (0-12 years)HeartCardiovascular systemConditions and diseasesAdult (19+)NA2009-12-04T05:00:00ZFraser Golding, MD, FRCPC11.000000000000045.0000000000000315.000000000000Flat ContentHealth A-Z<p>Learn about hypoplastic left heart syndrome (HLHS). This condition involves the left side of the heart being underdeveloped, and is extremely serious.</p><p>With hypoplastic left heart syndrome (HLHS), the left side of the heart is underdeveloped. Blood coming back to the heart from the lungs has to go through an atrial septal defect, and blood reaches the aorta through a patent ductus arteriosus. </p><h2> Key points </h2> <ul><li>Hypoplastic left heart syndrome (HLHS) is the most common severe congenital heart defect.</li> <li>Symptoms of HLHS usually appear soon after birth.</li> <li>HLHS cannot be corrected, but reconstructive heart surgery can usually help the baby live and grow. </li> <li>HLHS can be fatal if untreated, but survival improves after each surgery for the condition.</li></ul>
Hypoplasie du cœur gaucheHHypoplasie du cœur gaucheHydoplastic Left Heart Syndrome (HLHS)FrenchCardiologyChild (0-12 years)HeartCardiovascular systemConditions and diseasesAdult (19+)NA2009-12-04T05:00:00ZFraser Golding, MD, FRCPC11.000000000000045.0000000000000315.000000000000Flat ContentHealth A-Z<p>Informez-vous sur l’hypoplasie du coeur gauche. Cette anomalie extrêmement grave fait en sorte que le côté gauche du cœur est sous-développé.</p><p>L’hypoplasie du cœur gauche fait en sorte que le côté gauche du cœur est sous-développé. Le sang revenant dans le cœur à partir des poumons doit passer dans une communication interauriculaire, et le sang atteint l’aorte par l’intermédiaire d’une persistance du canal artériel.<br></p><h2>À retenir </h2> <ul><li> L’hypoplasie du cœur gauche est la plus commune des anomalies cardiaques congénitales graves. </li> <li> Les symptômes deviennent habituellement visibles peu après la naissance. </li> <li> L’hypoplasie du cœur gauche ne peut être corrigée, mais une chirurgie cardiaque reconstructive peut habituellement aider le bébé à vivre et à grandir. </li> <li> Ce trouble peut être mortel s’il n’est pas traité, mais le taux de survie s’améliore avec chaque intervention chirurgicale. </li></ul>

 

 

Hypoplastic left heart syndrome (HLHS)1614.00000000000Hypoplastic left heart syndrome (HLHS)Hypoplastic left heart syndrome (HLHS)HEnglishCardiologyChild (0-12 years)HeartCardiovascular systemConditions and diseasesAdult (19+)NA2009-12-04T05:00:00ZFraser Golding, MD, FRCPC11.000000000000045.0000000000000315.000000000000Flat ContentHealth A-Z<p>Learn about hypoplastic left heart syndrome (HLHS). This condition involves the left side of the heart being underdeveloped, and is extremely serious.</p><p>With hypoplastic left heart syndrome (HLHS), the left side of the heart is underdeveloped. Blood coming back to the heart from the lungs has to go through an atrial septal defect, and blood reaches the aorta through a patent ductus arteriosus. </p><h2> Key points </h2> <ul><li>Hypoplastic left heart syndrome (HLHS) is the most common severe congenital heart defect.</li> <li>Symptoms of HLHS usually appear soon after birth.</li> <li>HLHS cannot be corrected, but reconstructive heart surgery can usually help the baby live and grow. </li> <li>HLHS can be fatal if untreated, but survival improves after each surgery for the condition.</li></ul><p>HLHS is the most common of the severe congenital heart defects. It accounts for 7% to 9% of all heart defects diagnosed within the first year of life. </p> <figure class="swf-asset-c-80"> <span class="asset-image-title">Hypoplastic left heart syndrome</span> <div class="asset-animation"> src="https://akhpub.aboutkidshealth.ca/Style%20Library/akh/swfanimations/swf.html?swffile=Hypoplastic_left_heart_syndrome_MED_ANI_EN.swf" </div> <figcaption class="asset-image-caption">The left side of the heart is underdeveloped and a hole in the upper chambers of the heart results in oxygen-rich blood leaking into the right atrium. A patent ductus arteriosus allows mixed blood to flow from the pulmonary vessels into the aorta and allows some oxygen to reach the body.</figcaption> </figure> <h2>What are the symptoms of hypoplastic left heart syndrome?</h2><p>Symptoms usually become noticeable soon after birth when the ductus ateriosus closes. They include cyanosis, poor colour, rapid difficult breathing, and trouble eating. The condition can be fatal if left untreated. An electrocardiogram and an echocardiogram are done to make a diagnosis. </p><h2>How is hypoplastic left heart syndrome treated?</h2><p>At first, a drug like prostaglandin will be given to keep the ductus arteriosus open to improve blood flow. HLHS cannot be corrected, but reconstructive heart surgery can usually help the baby live and grow. Three operations are done in stages, to help the body and lungs adjust to the altered blood flow. They include:</p><ul><li>the Norwood procedure</li><li>the bidirectional cavopulmonary shunt(BCPS)</li><li>the Fontan operation</li></ul><p>The goal is to help the right ventricle pump only oxygenated blood to the body and prevent it from mixing with de-oxygenated blood. </p><p>Heart transplantation may also be considered as an alternative surgical option. </p><h2>What is the long-term outlook for children with hypoplastic left heart syndrome?</h2><p>It is estimated that 75% of children with HLHS survive after the first stage of the reconstruction. Survival improves with each subsequent surgical procedure. </p>Hypoplastic left heart syndrome (HLHS)

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