Morphea of the faceMMorphea of the faceMorphea of the faceEnglishDermatologyChild (0-12 years);Teen (13-18 years)Head;SkinSkinConditions and diseasesCaregivers Adult (19+)NA2019-06-06T04:00:00ZElena Pope, MD, MSc, FRCPC;Ronald M. Laxer, MD, FRCPC;Christine O'Brien, BSc, OT Reg (Ont), MSc7.9000000000000063.00000000000001160.00000000000Health (A-Z) - ConditionsHealth A-Z<p>Morphea is a rare condition in which the skin becomes thick and hard due to excess collagen deposition.<br></p><h2>What is morphea of the face?</h2> <p>Morphea is a skin condition also known as localized scleroderma, meaning "hard skin." The skin becomes thick and hard because it contains too much collagen and other proteins. </p> <p>There are two types of scleroderma: a systemic type and a localized type. Localized scleroderma must not be confused with systemic scleroderma. The localized type affects the skin only and does not affect the internal organs. </p> <p>When this condition appears on the face, it is called "morphea of the face." <br></p><h2>Key points</h2><ul><li>Morphea is an uncommon condition that causes the skin to harden.</li><li>Morphea of the face is treated with creams and/or oral medications.</li> <li>The active inflammation phase of morphea of the face stops after several years.</li></ul><h2>Morphea looks like discoloured patches on the skin</h2> <p>Morphea makes patches called "plaques" or "lesions" on the skin. It usually begins with a reddish patch that, over time, becomes waxy white with a purple border. It often has the appearance of a bruise. However, it can look very different from person to person.<br></p><ul> </ul> <p>As morphea progresses, the affected skin may change. The veins under the skin may show more clearly. The affected skin may look thinner, and may look raised or sunken compared to the skin around it. </p><h2>Morphea has no known cause</h2> <p>Sometimes morphea seems to happen after an injury. Morphea likely results from an overactive immune system (autoimmune disease). Morphea is not contagious. </p><h2>Morphea is diagnosed by history and examination</h2> <p>The doctor might take a small part of the skin to send to the lab for tests. This is called a biopsy. There is no blood test to confirm the diagnosis of morphea, although the doctors will ask for tests to look for functioning of other organs. </p><h2>There are several treatments for morphea</h2><p>Morphea can be treated, but it cannot be cured. Treatment can reduce the inflammation, stop lesions from spreading and prevent new lesions from appearing. </p><h3>Creams, ointments and medication</h3><p>You may be given ointments or creams to put on your child's skin.</p><p>Your child may need stronger medication, such as <a href="/Article?contentid=221&language=English">prednisone</a> or <a href="/Article?contentid=185&language=English">methotrexate</a>, if the morphea:  </p><ul><li>starts at a younger age</li><li>affects large areas</li><li>is spreading rapidly</li></ul><p>Your child may need to have regular blood tests in these cases. These tests monitor the effects and possible side effects of the medication. Occasionally, other medicine may be needed as well.<br></p><h3>Cosmetics</h3><p>There are special make-up products that can cover the darker or lighter parts of the skin. Ask your doctor about these products.</p><h3>Monitoring</h3><p>At each clinic visit, your child's skin will be examined. Photographs will be taken to help keep track of changes in the morphea.</p><p>Ultrasound or MRI may be used to see if the morphea has affected the deeper tissues under the skin and to look for associated changes in the brain.</p><h3>Cosmetic surgery</h3><p>Some children with morphea of the face may be candidates for plastic surgery and can be referred for a consultation.</p><h2>Skin changes</h2><p>When the disease becomes inactive, the affected skin may become darker (or occasionally lighter) than the rest of the skin. Additionally, hardening of the skin may leave permanent scarring. Loss of fat may make the skin appear thinner with more visible vessels.</p><h2>Cosmetic impact</h2><p>Morphea may cause the affected side of the face to look smaller. The difference in size compared with the normal side may become more obvious when the child grows, even if the disease is no longer active.</p><h2>Hair loss</h2><p>If the morphea affects the scalp, it may lead to hair loss that is permanent in most cases.</p><h2>Associated brain changes</h2><p>Some children may experience headaches. Rarely, complications such as seizures and brain inflammation may happen. Your doctor may ask for an MRI of the brain to see if any changes are present. Some changes, such as calcium deposits, do not have any associated symptoms.</p><h2>Associated eye changes</h2><p>Some children may have inflammation of the eye, even if they do not have any symptoms. The doctor will recommend an eye exam.</p><h2>Associated mouth and dental changes</h2><p>In some children, especially with Parry-Romberg Syndrome, differences in the size and growth of the mouth may occur. These children may require orthodontic treatment.</p><p>If your child is on methotrexate or prednisone and becomes unwell, has fever or has been exposed to chickenpox and is not vaccinated, stop the medication and contact your child’s health-care team for further information.</p><p>If your child has seizures or become weak, take them to the nearest emergency department and notify their health-care team.</p>
Morphée du visageMMorphée du visageMorphea of the faceFrenchDermatologyChild (0-12 years);Teen (13-18 years)Head;SkinSkinConditions and diseasesCaregivers Adult (19+)NA2019-06-06T04:00:00ZElena Pope, MD, MSc, FRCPC;Ronald M. Laxer, MD, FRCPC;Christine O'Brien, BSc, OT Reg (Ont), MScHealth (A-Z) - ConditionsHealth A-Z<p>La morphée est un trouble rare caractérisé par l’épaississement et le durcissement de la peau en raison de l’excès de collagène qui y est déposé.</p><h2>Qu’est-ce que la morphée du visage?</h2><p>La morphée est une maladie de la peau connue sous le nom de sclérodermie localisée qui signifie « peau dure ». La présence de collagène et d’autres protéines en quantité excessive dans la peau cause son épaississement et son durcissement.</p><p>Il existe deux types de sclérodermie, soit la forme systémique et la forme localisée. Il ne faut pas confondre un type avec l’autre; la forme localisée se limite à la peau et les organes internes sont exempts de la maladie.</p><p>Quand la maladie s’attaque au visage, on l’appelle « morphée du visage ».</p><h2>À retenir</h2><ul><li>La morphée est un trouble peu courant qui provoque le durcissement de la peau.</li><li>La maladie se traite au moyen de crèmes ou d’onguents, ou par l’administration de médicaments oraux.</li><li>La phase d’inflammation active de la maladie qui s’attaque au visage s’éteint après quelques années.</li></ul><h2>La peau présente des plaques décolorées caractéristiques de la maladie</h2><p>Des plaques ou des lésions apparaissent sur la peau. En général, on observe, au début, une plaque légèrement rougie qui, au fil du temps, blanchit et prend une apparence cireuse bordée de violet. Elle se confond souvent avec une lésion. Son apparence peut cependant varier d’une personne à l’autre. </p><p>La peau change au fur et à mesure que la maladie progresse. Les veines sous la peau peuvent devenir visibles. La peau peut sembler plus mince et soulevée ou enfoncée par endroits.</p><h2>La morphée est rare et la cause n’est pas connue</h2><p>La maladie semble parfois survenir à la suite d’un accident et résulte selon toute vraisemblance de l’hyperactivité du système immunitaire (maladie auto-immune). La maladie n’est pas contagieuse.</p><h2>Le diagnostic de la morphée est effectué au moyen de l’examen et de la recherche des antécédents médicaux</h2><p>Il se peut que le médecin prélève de petits morceaux de peau et les envoie au laboratoire pour des tests (biopsie). Aucune analyse sanguine ne permet de confirmer le diagnostic de la morphée bien que le médecin procédera à des tests pour vérifier le fonctionnement des autres organes.</p><p>La morphée peut être traitée, mais elle ne se guérit pas. Le traitement peut réduire l’inflammation, freiner la propagation des lésions et prévenir l’apparition de nouvelles lésions.</p><h3>Crèmes, onguents et médicaments</h3><p>Des crèmes ou des onguents en application topique peuvent être recommandés à votre enfant.</p><p>Des médicaments plus puissants comme la <a href="/Article?contentid=221&language=French">prednisone</a> ou le <a href="/Article?contentid=185&language=French">méthotrexate</a> peuvent être prescrits si nécessaire à votre enfant dans le cas où la morphée :</p><ul><li>atteint l’enfant dès son jeune âge</li><li>couvre de très grandes surfaces du corps</li><li>se propage rapidement</li></ul><p>Il pourrait s’avérer nécessaire dans ces cas de pratiquer des analyses sanguines régulièrement pour surveiller l’efficacité ou les effets secondaires des médicaments. Il pourrait également y avoir lieu de prescrire d’autres médicaments.</p><h3>Produits cosmétiques</h3><p>Des produits de maquillage particuliers peuvent être utilisés pour couvrir des surfaces plus claires ou foncées de la peau. Demandez à votre médecin.</p><h3>Surveillance</h3><p>La peau de votre enfant sera examinée lors de chaque visite à la clinique. Des photos seront prises pour suivre l’évolution de la maladie.</p><p>Les échographies ou l’IRM peuvent être utilisés pour vérifier si les tissus sous-cutanés sont atteints et s’il y a présence de modifications concomitantes du cerveau.</p><h3>Chirurgie esthétique</h3><p>Certains enfants qui sont atteints de la morphée du visage pourraient être aptes à subir une chirurgie plastique après avoir été aiguillés vers une consultation.</p><h2>Modifications de la peau</h2><p>Lorsque la maladie s’estompe, la peau touchée peut prendre une teinte foncée (ou plus pâle à l’occasion) par rapport aux zones voisines. De plus, le durcissement de la peau peut laisser des cicatrices permanentes. La perte de gras peut donner l’impression que la peau est plus mince et rendre les vaisseaux sanguins plus visibles.</p><h2>Effets cosmétiques</h2><p>Le côté du visage qui est affecté peut sembler se rétrécir. À mesure que l’enfant grandira, même si la maladie disparaît complètement, on pourra observer des différences de taille entre la surface touchée et la surface saine.</p><h2>Calvitie</h2><p>Si la morphée touche le cuir chevelu, une calvitie permanente dans la plupart des cas peut en résulter.</p><h2>Modifications concomitantes du cerveau</h2><p>Certains enfants peuvent éprouver des maux de tête. La maladie peut rarement donner lieu à des complications comme des convulsions et l’inflammation du cerveau. Il se peut que votre médecin demande une IRM du cerveau afin de vérifier s’il a pu subir des modifications. Certaines modifications, comme le dépôt de calcium, ne sont associées à aucun symptôme.</p><h2>Modifications oculaires concomitantes</h2><p>Certains enfants peuvent présenter une inflammation oculaire même s’ils n’ont aucun symptôme. Le médecin recommandera un examen des yeux.</p><h2>Modifications de la dentition et de la bouche concomitantes</h2><p>Certains enfants atteints du syndrome Parry-Romberg, peuvent présenter des différences dans la taille et la croissance de la bouche. Des soins orthodontiques peuvent s’avérer nécessaires pour ces enfants.</p><p>Dans le cas où l’on administre du méthotrexate ou de la prednisone à votre enfant et qu’il ne se sent pas bien, a de la fièvre ou qu’il a été exposé à la varicelle sans être vacciné, cessez de lui administrer les médicaments et communiquez avec l’équipe de soins de santé de votre enfant pour obtenir davantage de renseignements.</p><p>Si votre enfant a des convulsions ou s’affaiblit, emmenez-le au service des urgences le plus près et informez son équipe de soins de santé.</p>

 

 

 

 

Morphea of the face917.000000000000Morphea of the faceMorphea of the faceMEnglishDermatologyChild (0-12 years);Teen (13-18 years)Head;SkinSkinConditions and diseasesCaregivers Adult (19+)NA2019-06-06T04:00:00ZElena Pope, MD, MSc, FRCPC;Ronald M. Laxer, MD, FRCPC;Christine O'Brien, BSc, OT Reg (Ont), MSc7.9000000000000063.00000000000001160.00000000000Health (A-Z) - ConditionsHealth A-Z<p>Morphea is a rare condition in which the skin becomes thick and hard due to excess collagen deposition.<br></p><h2>What is morphea of the face?</h2> <p>Morphea is a skin condition also known as localized scleroderma, meaning "hard skin." The skin becomes thick and hard because it contains too much collagen and other proteins. </p> <p>There are two types of scleroderma: a systemic type and a localized type. Localized scleroderma must not be confused with systemic scleroderma. The localized type affects the skin only and does not affect the internal organs. </p> <p>When this condition appears on the face, it is called "morphea of the face." <br></p><h2>Morphea of the face</h2> <p>There are two types of morphea that can affect the face:</p> <ul> <li><em>En coup de sabre</em> (hit by the sabre) appears on the forehead and sometimes the scalp as a linear streak or sunken skin with pigmentation changes.</li> <li>Parry-Romberg Syndrome appears on the face below the forehead. This type of morphea affects the skin as well as the tissues under it. The colour of the skin might change, and the tissues underneath may appear sunken or smaller. If the morphea affects one side of the face, this side might look smaller than the other side. As the child grows, the difference in the size and shape of that part of the skin may become more obvious, even if there is no ongoing inflammation of the skin. </li> </ul><h2>Key points</h2><ul><li>Morphea is an uncommon condition that causes the skin to harden.</li><li>Morphea of the face is treated with creams and/or oral medications.</li> <li>The active inflammation phase of morphea of the face stops after several years.</li></ul><h2>Morphea looks like discoloured patches on the skin</h2> <p>Morphea makes patches called "plaques" or "lesions" on the skin. It usually begins with a reddish patch that, over time, becomes waxy white with a purple border. It often has the appearance of a bruise. However, it can look very different from person to person.<br></p><ul> </ul> <p>As morphea progresses, the affected skin may change. The veins under the skin may show more clearly. The affected skin may look thinner, and may look raised or sunken compared to the skin around it. </p><h2>Morphea has no known cause</h2> <p>Sometimes morphea seems to happen after an injury. Morphea likely results from an overactive immune system (autoimmune disease). Morphea is not contagious. </p><p>The disease is unpredictable. Most children have the disease for months and even years before it becomes recognized or diagnosed. Even without treatment, morphea stops being active and it usually “burns out” after three to five years. </p><p>The disease has three phases:</p><ul><li>an early inflammatory phase that presents as nonspecific redness </li><li>an ongoing active phase, which typically presents with a hardened middle of white discolouration with a red-purple border<br></li><li>a burnt-out phase, appearing as increased colour, thinning of the skin with more visible vessels or sunken skin layers (due to loss of fat)</li></ul><h2>Morphea is diagnosed by history and examination</h2> <p>The doctor might take a small part of the skin to send to the lab for tests. This is called a biopsy. There is no blood test to confirm the diagnosis of morphea, although the doctors will ask for tests to look for functioning of other organs. </p><h2>There are several treatments for morphea</h2><p>Morphea can be treated, but it cannot be cured. Treatment can reduce the inflammation, stop lesions from spreading and prevent new lesions from appearing. </p><h3>Creams, ointments and medication</h3><p>You may be given ointments or creams to put on your child's skin.</p><p>Your child may need stronger medication, such as <a href="/Article?contentid=221&language=English">prednisone</a> or <a href="/Article?contentid=185&language=English">methotrexate</a>, if the morphea:  </p><ul><li>starts at a younger age</li><li>affects large areas</li><li>is spreading rapidly</li></ul><p>Your child may need to have regular blood tests in these cases. These tests monitor the effects and possible side effects of the medication. Occasionally, other medicine may be needed as well.<br></p><h3>Cosmetics</h3><p>There are special make-up products that can cover the darker or lighter parts of the skin. Ask your doctor about these products.</p><h3>Monitoring</h3><p>At each clinic visit, your child's skin will be examined. Photographs will be taken to help keep track of changes in the morphea.</p><p>Ultrasound or MRI may be used to see if the morphea has affected the deeper tissues under the skin and to look for associated changes in the brain.</p><h3>Cosmetic surgery</h3><p>Some children with morphea of the face may be candidates for plastic surgery and can be referred for a consultation.</p><h2>Skin changes</h2><p>When the disease becomes inactive, the affected skin may become darker (or occasionally lighter) than the rest of the skin. Additionally, hardening of the skin may leave permanent scarring. Loss of fat may make the skin appear thinner with more visible vessels.</p><h2>Cosmetic impact</h2><p>Morphea may cause the affected side of the face to look smaller. The difference in size compared with the normal side may become more obvious when the child grows, even if the disease is no longer active.</p><h2>Hair loss</h2><p>If the morphea affects the scalp, it may lead to hair loss that is permanent in most cases.</p><h2>Associated brain changes</h2><p>Some children may experience headaches. Rarely, complications such as seizures and brain inflammation may happen. Your doctor may ask for an MRI of the brain to see if any changes are present. Some changes, such as calcium deposits, do not have any associated symptoms.</p><h2>Associated eye changes</h2><p>Some children may have inflammation of the eye, even if they do not have any symptoms. The doctor will recommend an eye exam.</p><h2>Associated mouth and dental changes</h2><p>In some children, especially with Parry-Romberg Syndrome, differences in the size and growth of the mouth may occur. These children may require orthodontic treatment.</p><p>Discuss the diagnosis openly with your child and provide reassurance.</p><p>Discuss the diagnosis with teachers, especially if your child would require multiple hospital visits and treatments and to prevent bullying.</p><p>Seek reassurance and coping strategies from your child’s health-care team and ask for a referral to a mental health specialist if your child is becoming anxious or depressed or is facing bullying.</p><p>Most of the complications related to the disease can be decreased by treating it early. Follow the health-care team’s recommendations for screening of associated complications (eye, brain, psychological).</p><p>If your child is on methotrexate or prednisone and becomes unwell, has fever or has been exposed to chickenpox and is not vaccinated, stop the medication and contact your child’s health-care team for further information.</p><p>If your child has seizures or become weak, take them to the nearest emergency department and notify their health-care team.</p><h2>Outcome</h2> <p>The active inflammation phase of morphea of the face usually lasts about three to five years. The majority of children recover well from morphea of the face. </p> <p>After the morphea is gone, there may be some change in the pigment (colour) of the skin. </p> <p>The skin and other tissues may atrophy (shrink). The fatty tissue under the skin may disappear. This will make affected areas look thinner and have a different texture. </p>Morphea of the faceFalse