|Cardiomyopathie hypertrophique||C||Cardiomyopathie hypertrophique||Hypertrophic Cardiomyopathy||French||Cardiology||Child (0-12 years);Teen (13-18 years)||Heart||Cardiovascular system||Conditions and diseases||Adult (19+)||NA||2010-01-15T05:00:00Z||Jennifer Russell, MD, FRCPC||11.0000000000000||38.0000000000000||222.000000000000||Flat Content||Health A-Z||<p>Informez-vous sur la myocardiopathie hypertrophique, un épaississement exceptionnel du muscle cardiaque qui peut affecter la quantité de sang pompé ves le cœur et causer de l’arythmie.</p>||<p>Cette page explique en quoi la myocardiopathie hypertrophique influence la capacité du coeur à pomper, à se décontracter normalement, et à faire circuler le sang dans le corps. </p>||<h2> À retenir </h2>
<ul><li> En présence de myocardiopathie hypertrophique, le muscle cardiaque est exceptionnellement épais et le coeur a donc du mal à pomper du sang vers le corps. </li>
<li>La cardiomyopathie hypertrophique est normalement héréditaire. </li>
<li> Les médecins recommandent de recourir à un défibrillateur cardiaque implantable (DCI) lorsque l’épaisseur du cœur atteint une taille déterminée.
|Hypertrophic cardiomyopathy||H||Hypertrophic cardiomyopathy||Hypertrophic cardiomyopathy||English||Cardiology||Child (0-12 years);Teen (13-18 years)||Heart||Cardiovascular system||Conditions and diseases||Adult (19+)||NA||2018-10-26T04:00:00Z||Jennifer Russell, MD, FRCPC;Aamir Jeewa, MD, FAAP, FRCP(C)||11.0000000000000||38.0000000000000||222.000000000000||Health (A-Z) - Conditions||Health A-Z||<p>Hypertrophic cardiomyopathy is a condition in which the heart muscle is unusually thick. This can affect the amount of blood pumped to the body and cause heart rhythm problems.</p>||<figure class="swf-asset-c-80"><span class="asset-image-title">Hypertrophic cardiomyopathy</span>
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<figcaption class="asset-image-caption">With this condition, the muscle in the heart is unusually thick. This can reduce the size of the left ventricle or make the walls of the ventricle stiffer, which affects the ability of the heart to pump and relax effectively and send blood to the body.</figcaption> </figure>
<p>For patients with hypertrophic cardiomyopathy (HCM), the muscle in the heart, usually in <a href="/Article?contentid=1577&language=English">the ventricles</a>, is unusually thick. This is known as hypertrophy. This can reduce the size of the left ventricle or make the walls of the ventricle stiffer, which affects the ability of the heart to pump and relax effectively and send blood to the body and/or the lungs. The altered arrangement of muscle fibres from the thickened muscle can cause abnormal heart rhythms, which are potentially fatal. HCM can develop at any age.</p>||<h2>Key points</h2><ul><li>With hypertrophic cardiomyopathy, the muscle in the heart is unusually thick, affecting its ability to pump blood to the body.</li><li>This condition is usually genetic and passed through families.</li><li>Doctors may recommend an implantable cardioverter defibrillator (ICD) to treat this condition when the heart thickness reaches a certain size.<br></li></ul>||<h2>Symptoms of HCM in children</h2><p>Symptoms of HCM include: </p><ul><li>shortness of breath</li><li>chest pain</li><li>dizziness</li><li>fainting </li><li>cardiac arrest (only in some cases). </li></ul><p>Some people with HCM may not experience any symptoms for a long time. <br></p>||<h2>What causes HCM in babies and children?</h2><p>HCM can occur spontaneously, however most often, the cause is genetic, meaning it is passed along through families. For this reason, it is usually recommended that anyone who is a first-degree relative (parent, sibling, or child) of someone with HCM have a cardiac evaluation even if they do not have any health concerns or heart-related symptoms.</p><p>Hypertrophic cardiomyopathy is less common in babies and children and more often diagnosed during adolescence. It occurs in 1 in every 500 people.</p>||<h2>Treatment of HCM</h2><p>Implantable cardiac defibrillators (ICD) are recommended when the heart thickness reaches a certain size, even in the absence of abnormal heart rhythms (arrhythmias). ICDs may reduce the risk of significant arrhythmias in certain types of hypertrophic cardiomyopathy patients.</p><p>Many children will be on beta blocker medicine, a type of medicine that is used to slow the heart rate and ease the workload of the heart. On rare occasions, this condition may require a heart transplant.</p>||<h2>Complications of HCM</h2><p>HCM has been associated with sudden cardiac events in children and adolescents often due to either the blockage of blood getting out of the heart or an abnormally fast heart rhythm (arrhythmia). HCM is one of the most common causes of sudden death in young athletes. Arrhythmias have been seen in up to 30-40% of patients with HCM and ongoing research shows this may be related to the healthy normal heart muscle (or myocardium) being replaced by abnormal tissue called myocardial fibrosis. Infants with HCM may also have an underlying metabolic condition that may involve other muscle groups or organs.</p>|